Czech and Slovak Ophthalmology 474 Original article Eye Manifestation of Extrarenal Malignant Rhabdoid Tumour Prívarová Eva Griščíková Lenka Lokaj Martin Vokurková Jitka Mazánek Jiří Autrata Rudolf https://orcid.org/0000-0002-2689-882X 22 4 2014 2 5

Extrarenal malignant rhabdoid tumour (EMRT) is very rare and aggresive childhood neoplasm with a rapid progression. The prognosis is still very poor with 80 % mortality rate. We report a case of a newborn baby with extrarenal malignant rhabdoid tumour of an upper eyelid. An EMRT was diagnosed based on the histological examination. This case report highlights the clinical presentation, radiological features and difficulty in diagnosis. The purpose is to underline the importance of its inclusion in the differential diagnosis of any aggresive lesion in a child.

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